Development of a Functional Assessment Scale for Ambulatory Boys with Duchenne Muscular Dystrophy

Elaine Scott; Michelle Eagle; Anna Mayhew; Jenny Freeman; Marion Main; Jennie Sheehan; Adnan Manzur; Francesco Muntoni

doi:10.1002/pri.520

journal article Sep 23, 2011

Development of a Functional Assessment Scale for Ambulatory Boys with Duchenne Muscular Dystrophy

Elaine Scott Michelle Eagle Anna Mayhew Jenny Freeman Marion Main Jennie Sheehan Adnan Manzur Francesco Muntoni

Physiotherapy Research International Vol. 17 No. 2 pp. 101-109 · Wiley

View at Publisher Save 10.1002/pri.520

Abstract

AbstractBackground and PurposeThe aims of this study were to develop a clinical assessment scale to measure functional ability in ambulant boys with Duchenne muscular dystrophy and to determine the reliability of the scale in multiple centres in the UK.MethodsFocus groups and workshops were held with experienced paediatric neuromuscular physiotherapists to determine scale content. A manual was prepared with accompanying videos, and training sessions were conducted. A total of 17 physiotherapists from participating centres used the videos to determine inter‐rater reliability. Five determined the intra‐rater reliability.ResultsStrength of agreement for these groups based on total subject scores was very good (0.95 and ≥0.93 for consistency and absolute agreement, respectively). Test–retest ability was high, with perfect agreement between occasions for all but two items of the scale.ConclusionsOur study indicates that the North Star Ambulatory Assessment is practical and reliable. It takes only 10 minutes to perform and incorporates both universally used timed tests as well as levels of activities, which allow assessment of high‐functioning boys with Duchenne muscular dystrophy. Copyright © 2011 John Wiley & Sons, Ltd.

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References

Details

Published: Sep 23, 2011
Vol/Issue: 17(2)
Pages: 101-109
License: View

Authors

E

Elaine Scott

Muscular Dystrophy Campaign London UK

M

Michelle Eagle

Institute of Human Genetics Newcastle UK

A

Anna Mayhew

Institute of Human Genetics Newcastle UK

J

Jenny Freeman

University of Sheffield Sheffield UK

M

Marion Main

Great Ormond Street Hospital London UK

J

Jennie Sheehan

Evelina Children's Hospital London UK

A

Adnan Manzur

Dubowitz Neuromuscular Centre Institute of Child Health, UCL London UK

F

Francesco Muntoni

Dubowitz Neuromuscular Centre Institute of Child Health, UCL London UK

Cite This Article

Elaine Scott, Michelle Eagle, Anna Mayhew, et al. (2011). Development of a Functional Assessment Scale for Ambulatory Boys with Duchenne Muscular Dystrophy. Physiotherapy Research International, 17(2), 101-109. https://doi.org/10.1002/pri.520

Development of a Functional Assessment Scale for Ambulatory Boys with Duchenne Muscular Dystrophy

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